Radiological Findings of a Large Dermatofibrosarcoma Protuberans with Pathological Correlation
A Bansal, KL Chakraborti, S Mahajan, S Soni, N Wadhwa
Hong Kong J Radiol 2013;16:307-11
DOI: 10.12809/hkjr1312106
Dermatofibrosarcoma protuberans is a rare, low- to intermediate-grade soft tissue sarcoma that is fibrohistiocytic in nature and originates from the dermis. Dermatofibrosarcoma protuberans is a locally aggressive tumour that invades deep subcutaneous tissues and has high recurrence rates. Radiological investigation is important to narrow down the differential diagnoses and to evaluate the local extent, particularly the level of infiltration of the tumour. Tumour infiltration is important for preoperative planning, especially for large tumours, as clinical examination alone may not be completely accurate and local recurrence is common, particularly for tumours with inadequately resected margins. Magnetic resonance imaging, with its superior soft tissue contrast, is particularly helpful. This report is of a patient with a large dermatofibrosarcoma protuberans on the right side of the anterior abdominal wall, and describes the radiological appearance and histopathological correlation.
中文摘要
巨大隆突性皮膚纖維肉瘤的放射學表現及其與病理學的相關性
A Bansal, KL Chakraborti, S Mahajan, S Soni, N Wadhwa
隆突性皮膚纖維肉瘤是一種罕見的低到中度惡性軟組織肉瘤，性質屬纖維組織細胞，起源於真皮層。它是一種侵入深層皮下組織的局部侵襲性腫瘤，復發率高。放射學檢查對縮小鑑別診斷範圍，評估腫瘤的局部範圍，尤其是浸潤程度很重要。腫瘤浸潤度對術前計劃相當重要，尤其對大體積腫瘤而言；單靠臨床評估可能不完全準確，同時局部復發很常見，特別對切除邊緣不完全的腫瘤。磁共振成像軟組織對比度高，特別有助於評估。本文報告一宗右腹前壁巨大隆突性皮膚纖維肉瘤的病例，並描述其放射性影像，以及其組織病理學相關性。